Journal article

Authors list: Neuhaeuser, Christoph Armin; Kreymborg, Karsten Grosse; Mueller, Carsten; Khalil, Markus; Jux, Christian; Galambos, Csaba; Schranz, Dietmar

Publication year: 2021

Pages: 228-231

Journal: Journal of Pediatric Intensive Care

Volume number: 10

Issue number: 03

ISSN: 2146-4618

eISSN: 2146-4626

Open access status: Green

DOI Link: https://doi.org/10.1055/s-0040-1713437

Publisher: Thieme Publishing

Abstract: 
A newborn infant patient presented with persistent pulmonary hypertension. For right ventricular decompression, the ductus arteriosus was kept open by prostaglandin E-1 infusion and was stented at the age of 4 weeks during heart catheterization. The child was weaned from mechanical ventilation, since pulmonary functions were adequate. A small atrial septal defect was identified and closed in cardiac catheterization laboratory to decrease preductal hypoxemia. Diagnostic workup led to the diagnosis of alveolar capillary dysplasia with misalignment of the pulmonary veins. Suprasystemic pulmonary arterial hypertension with persisting nitric oxide dependency remained the leading symptoms. The child underwent bilateral lung transplantation at the age of 28 months. He is well at the age of 44 months.

Harvard Citation style: Neuhaeuser, C., Kreymborg, K., Mueller, C., Khalil, M., Jux, C., Galambos, C., et al. (2021) Successful Management of an Infant with Atypical Presentation of Alveolar Capillary Dysplasia with Misalignment of the Pulmonary Veins, Journal of Pediatric Intensive Care, 10(03), pp. 228-231. https://doi.org/10.1055/s-0040-1713437

APA Citation style: Neuhaeuser, C., Kreymborg, K., Mueller, C., Khalil, M., Jux, C., Galambos, C., & Schranz, D. (2021). Successful Management of an Infant with Atypical Presentation of Alveolar Capillary Dysplasia with Misalignment of the Pulmonary Veins. Journal of Pediatric Intensive Care. 10(03), 228-231. https://doi.org/10.1055/s-0040-1713437